ICD 10 CM Codes

E71.0 Maple-syrup-urine disease
Billable Code  is a billable ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
GEMS
ICD-10-CM E71.0 converts approximately to:ICD-9-CM
2015 ICD-9-CM 270.3 Disturbances of branched-chain amino-acid metabolism
ICD-10-CM E71.0is grouped within Diagnostic Related Group(s) (MS-DRG v30.0)
642 INBORN AND OTHER DISORDERS OF METABOLISM
Alternate Description
Piebaldism
ICD-10-CM Index Entry
ICD-10-CM Index entries containing back-references to ICD-10-CM '.E71.0.'
Disease, diseased; maple-syrup-urine
Disorder (of); metabolism NOS; amino-acid; branched chain; maple syrup urine disease
Maple-syrup-urine disease
Menkes' disease or syndrome; meaning maple-syrup-urine disease
Syndrome; maple-syrup-urine