| Type 1 Excludes |
| disorders of: |
| aromatic amino-acid metabolism (E70.-) |
| branched-chain amino-acid metabolism (E71.0-E71.2) |
| fatty-acid metabolism (E71.3) |
| purine and pyrimidine metabolism (E79.-) |
| gout ( M1A-, M10.-) |
|
E72.0 |
Disorders of amino-acid transport |
|
E72.1 |
Disorders of sulfur-bearing amino-acid metabolism |
|
E72.2 |
Disorders of urea cycle metabolism |
|
E72.3 |
|
Disorders of lysine and hydroxylysine metabolism |
|
E72.4 |
|
Disorders of ornithine metabolism |
|
E72.5 |
Disorders of glycine metabolism |
|
E72.8 |
|
Other specified disorders of amino-acid metabolism |
|
E72.9 |
|
Disorder of amino-acid metabolism, unspecified |