Type 1 Excludes
- disorders of:
- aromatic amino-acid metabolism (E70.-)
- branched-chain amino-acid metabolism (E71.0-E71.2)
- fatty-acid metabolism (E71.3)
- purine and pyrimidine metabolism (E79.-)
- gout (M1A.-, M10.-)
- Codes Description
- E72.0
Disorders of amino-acid transport
- E72.1
Disorders of sulfur-bearing amino-acid metabolism
- E72.2
Disorders of urea cycle metabolism
- E72.3
Disorders of lysine and hydroxylysine metabolism
- E72.4
Disorders of ornithine metabolism
- E72.5
Disorders of glycine metabolism
- E72.8
Other specified disorders of amino-acid metabolism
- E72.9
Disorder of amino-acid metabolism, unspecified