| Type 1 Excludes |
| acrodermatitis enteropathica (E83.2) |
| congenital erythropoietic porphyria (E80.0) |
| pilonidal cyst or sinus (L05.-) |
| Sturge-Weber (-Dimitri) syndrome (Q85.8) |
|
Q82.0 |
|
Hereditary lymphedema |
|
Q82.1 |
|
Xeroderma pigmentosum |
|
Q82.2 |
|
Congenital cutaneous mastocytosis |
|
Q82.3 |
|
Incontinentia pigmenti |
|
Q82.4 |
|
Ectodermal dysplasia (anhidrotic) |
|
Q82.5 |
|
Congenital non-neoplastic nevus |
|
Q82.6 |
|
Congenital sacral dimple |
|
Q82.8 |
|
Other specified congenital malformations of skin |
|
Q82.9 |
|
Congenital malformation of skin, unspecified |